Table 5 Factors affecting survival
Risk factorRisk of death (95% CI)Level of evidenceReference
Dialysis dependence at diagnosisHR 8.2 (2.03 to 33.11) p = 0.0033Koldingsnes and Nossent 20029
VDI ⩾1 at diagnosisHR 5.54 (1.28 to 24.05) p = 0.0223Koldingsnes and Nossent 20029
Impaired renal function at diagnosisHR 5.10 (1.59–10.16)3Reinhold-Keller et al 200021
A serum albumin level of ⩽30 g/litre at diagnosisRR 4.5 (1.3 to 16)3Aasarod et al 20003
Renal involvement at diagnosis*HR 4.45 (1.48 to 13.65)3Reinhold-Keller et al 200021
Lung involvement at diagnosis†HR 3.74 (1.26 to 11.13)3Reinhold-Keller et al 200021
Age >52HR 3.4 (1.03 to 11.21), p = 0.043Bligny et al 20045
Age (rise of 10 years)HR 2.18 (1.38 to 3.42), p<0.0013Koldingsnes and Nossent 20029
Upper respiratory tract involvement at diagnosis‡HR 0.31 (0.11 to 0.84), p = 0.023Bligny et al 20045
  • *Affected only univariate analysis, not multivariate analysis.5 †Did not affect survival.5 ‡Affected only univariate analysis, not multivariate analysis.9

  • HR, hazard ratio; RR, relative risk; VDI, Vasculitis Damage Index.