Table 1

Characteristics of DM and PM subgroup as per ACR/EULAR criteria

DM (n=14)PM (n=12)
Mean age in years±SD46.3±12.840.3±10.8
Median time to diagnosis in months (IQR)8 (6.2–9.7)2 (1–3)
Female:male11:36:6
Organ system involved1412
 Muscle147
 Cutaneous1311
 Constitutional116
 Skeletal410
 Gastrointestinal88
 Pulmonary53
Severity of myositis at onset
 Mild21
 Moderate00
 Severe1211
Cutaneous manifestations
 Heliotrope rash5na
 Gottrons papule4na
 Gottrons sign11na
 Non-specific rash67
  • ACR/EULAR, American College of Rheumatology/European League Against Rheumatism; DM, dermatomyositis; na, not applicable; PM, polymyositis.